Anesthesia Management in Rare Case: Cutis Laxa Syndrome

  • Anahid Maleki Department of Anesthesiology and Critical Care, Medical Children Hospital, Tehran University of Medical Sciences, Tehran,Iran.
  • Alireza Ebrahim Soltani Department of Anesthesiology and Critical Care, Medical Children Hospital, Tehran University of Medical Sciences, Tehran,Iran.
  • Mehrdad Goudarzi Department of Anesthesiology and Critical Care, Medical Children Hospital, Tehran University of Medical Sciences, Tehran,Iran.
  • Amir Abbas Yaghooti Department of Anesthesiology and Critical Care, Bahrami Hospital,Tehran University of Medical Sciences, Tehran, Iran.
  • Abbas Ostad Alipour Department of Anesthesiology and Critical Care, Bahrami Hospital,Tehran University of Medical Sciences, Tehran, Iran
  • Ebrahim Espahbodi Department of Anesthesiology and Critical Care, Bahrami Hospital,Tehran University of Medical Sciences, Tehran, Iran
Keywords: Cutis laxa, pulmonary stenosis, loose skin

Abstract

Cutis laxa is rare and hetrogenous group of disorders related to abnormalities in elastic tissue. It may be autosomal recessive, autosomal dominant, X linked or acquired. Acquired cutis laxa has developed after a febrile illness, inflammatory skin disease such a lupus eryhymatosis or erythema multiform, amyloidosis, hypersensitivity reaction to penicillin and in infants born from women who were taking penicillamine. Patients with cutis laxa have facial features,.pulmonary emphysema, cor-pulmonale, and right-sided heart failure.We present a case with cutis laxa undescended testis , and mild  pulmonary stenosis.

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Published
2015-11-23
How to Cite
1.
Maleki A, Ebrahim Soltani A, Goudarzi M, Yaghooti AA, Ostad Alipour A, Espahbodi E. Anesthesia Management in Rare Case: Cutis Laxa Syndrome. AACC. 1(4):139-40.
Section
Case Report(s)