Archives of Anesthesiology and Critical Care 2015. 1(4):139-140.

Anesthesia Management in Rare Case: Cutis Laxa Syndrome
Anahid Maleki, Alireza Ebrahim Soltani, Mehrdad Goudarzi, Amir Abbas Yaghooti, Abbas Ostad Alipour, Ebrahim Espahbodi

Abstract


Cutis laxa is rare and hetrogenous group of disorders related to abnormalities in elastic tissue. It may be autosomal recessive, autosomal dominant, X linked or acquired. Acquired cutis laxa has developed after a febrile illness, inflammatory skin disease such a lupus eryhymatosis or erythema multiform, amyloidosis, hypersensitivity reaction to penicillin and in infants born from women who were taking penicillamine. Patients with cutis laxa have facial features,.pulmonary emphysema, cor-pulmonale, and right-sided heart failure.We present a case with cutis laxa undescended testis , and mild  pulmonary stenosis.

Keywords


Cutis laxa; pulmonary stenosis; loose skin

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