Tehran University of Medical Sciences Archives of Anesthesiology and Critical Care 2423-5849 7 3 2021 07 31 176 179 Haripriya Ramachandran Department of Paediatric Anaesthesia, Indira Gandhi Institute of Child Health, Rajiv Gandhi University of Health Sciences, Bengaluru, India. Dammaningala Bhagya Department of Paediatric Anaesthesia, Indira Gandhi Institute of Child Health, Rajiv Gandhi University of Health Sciences, Bengaluru, India.. 2021 04 23 2021 05 10 Cutis laxa is a rare congenital multisystem connective tissue disorder. Patients with cutis laxa have facial features, pulmonary emphysema and right-sided heart failure. Anaesthetic management is important because of difficult airway and respiratory/cardiac abnormalities. We have reported the preoperative evaluation and anaesthetic management of a child with Cutis laxa with right cleft lip and palate. https://aacc.tums.ac.ir/index.php/aacc/article/view/357