Tehran University of Medical Sciences Archives of Anesthesiology and Critical Care 2423-5849 9 3 2023 06 25 268 271 Sumaila Naaz Department of Anaesthesiology, SMS Hospital and Attached Hospitals, Jaipur, Rajasthan, India. Anjum Saiyed Department of Anaesthesiology, SMS Hospital and Attached Hospitals, Jaipur, Rajasthan, India. Reema Meena Department of Anaesthesiology, SMS Hospital and Attached Hospitals, Jaipur, Rajasthan, India. Arun Garg Department of Anaesthesiology, SMS Hospital and Attached Hospitals, Jaipur, Rajasthan, India. 2022 07 25 2022 08 27 Ebstein anomaly is a challenge to the anaesthetist in terms of large right atrium, atrialised right ventricle and various valve abnormalities associated with it like Tricuspid Regurgitation(TR), Mitral Stenosis(MS), Mitral Regurgitation(MR). In this case study, we report a 14-year-old female child presented with ebstein anomaly and cleft palate in our institution, SMS medical college & hospitals, Jaipur, Rajasthan. Cone’s operation was planned but due to multiple fenestrations in tricuspid leaflet only tricuspid and mitral valves were replaced. Patient was extubated next day with uneventful recovery. https://aacc.tums.ac.ir/index.php/aacc/article/view/615