Anesthesia and Airway Management of a Patient with Sturge- Weber Syndrome Associated with Extreme Ocular Manifestations and Giant Facial Hemangioma

Tehran University of Medical Sciences Archives of Anesthesiology and Critical Care 2423-5849 2 3 2016 08 10 Anesthesia and Airway Management of a Patient with Sturge- Weber Syndrome Associated with Extreme Ocular Manifestations and Giant Facial Hemangioma 231 233 EN Mahtab Poor Zamany Nejat Kermany Department of Anesthesiology and Critical Care, Labbafinejad Medical Center, Shahid Beheshti Medical Center, Tehran, Iran Badiozaman Radpay Department of Anesthesiology and Critical Care, Shohada Tajrish Medical Center, Shahid Beheshti Medical Center, Tehran, Iran 2016 07 31 2016 07 31 Sturge-Weber syndrome (SWS) is a very rare congenital disorder that is manifested by facial capillary malformation (port wine stain) which may be associated with capillary – venous malformations affecting many parts such as the brain, eyes facial skin and mucosa and also airways. In this report we present an unusual 28 years old female case of SWS that presented with signs and symptoms of sudden increased intra ocular pressure (exacerbation of glaucoma) and manifestations of facial and airway involvement. A discussion about anesthetic and airway management of such patient follow the case presentation. https://aacc.tums.ac.ir/index.php/aacc/article/view/83 https://aacc.tums.ac.ir/index.php/aacc/article/download/83/217