The Hidden Arch: An Incidental Vascular Surprise in a Toddler Undergoing Cleft Palate Repair
Abstract
Double aortic arch (DAA) is a rare congenital vascular anomaly that forms a complete vascular ring encircling the trachea and esophagus, potentially leading to respiratory and feeding difficulties. We present a case of a 15-month-old male with an incomplete cleft palate who had an incidental finding of codominant double arch of aorta on preoperative imaging. The child underwent successful cleft palate surgery under general anesthesia with appropriate airway precautions and multidisciplinary planning. This report highlights the anesthetic implications of vascular rings and the need for thorough preoperative assessment in children presenting with non-specific symptoms like recurrent upper respiratory tract infections (URTI) and feeding intolerance.
[2] Hernanz-Schulman M. Vascular rings: a practical approach to imaging diagnosis. Pediatr Radiol. 2005;35(10):961-79.
[3] van Son JA, Julsrud PR, Hagler DJ, Sim EK, Pairolero PC, Puga FJ, et al. Surgical treatment of vascular rings: the Mayo Clinic experience. Mayo Clin Proc. 1993; 68(11):1056-63.
[4] Humphrey C, Duncan K, Fletcher S. Decade of experience with vascular rings at a single institution. Pediatrics. 2006; 117(5):e903-8.
[5] Backer CL, Mavroudis C, Rigsby CK, Holinger LD. Trends in vascular ring surgery. J Thorac Cardiovasc Surg. 2005;129(6):1339-1347.
[6] Wadle M, Joffe D, Backer CL, Ross F. Perioperative and anaesthetic considerations in vascular rings and slings. Semin Cardiothorac Vasc Anesth. 2024;28(3):152-164.
[7] Worhunsky DJ, Levy BE, Stephens EH, Backer CL. Vascular rings. Semin Pediatr Surg. 2021;30(6):151128.
[8] Sekhon PS, Ethunandan M, Markus AF, Krishnan G, Rao CB. Congenital anomalies associated with cleft lip and palate: an analysis of 1623 consecutive patients. Cleft Palate Craniofac J. 2011;48(4):371-378.
[9] Berdon WE. Vascular rings: anomalies of the aortic arch. In: Caffey’s Pediatric Diagnostic Imaging. 10th ed. Mosby; 2004. p. 1226–1231.
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| Issue | Article in Press |
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| Section | Case Report(s) | |
| Keywords | ||
| paediatrics congenital anomalies cleft palate pre anesthetic evaluation | ||
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