Case Report

Anesthetic Management of a Parturient with Spinal Muscle Atrophy for Cesarean Section: A Case Report

Abstract

Spinal muscular atrophy is a rare genetic neuromuscular disease characterized by loss of anterior horn cells of spinal cord and brain stem nuclei, resulting in progressive muscle weakness. Anesthesia for these patients is risky because of the risk of worsening of muscle weakness and consequent postoperative respiratory complications. We report anesthesia management in a nulliparous parturient with type 3 disease who underwent urgent cesarean delivery due to progressive decline of amniotic fluid index.

[1] Abati E, Corti S. Pregnancy outcomes in women with spinal muscular atrophy: A review. J Neurol Sci. 2018; 388:50-60.
[2] Bollag L, Kent C, Richebé Ph, Landau R. Anesthetic management of spinal muscle atrophy type II in a parturient. Local Reg Anesth. 2011; 4: 15–20.
[3] Golden S. Labor analgesia and anesthesia in a patient with spinal muscular atrophy and vocal cord paralysis. Reg Anesth. 1997;2 2(6):595-6.
[4] Alman KG, Wilson IA (eds). Oxford handbook of anaesthesia. 2nd ed. Oxford: Churchill Livingstone, 2006: 314.
[5] Gac M, Kokot N, Koziolek A, Kuczkowski KM. Combined spinal epidural anesthesia for cesarean section in a parturient with spinal muscle atrophy type III (Kugelberg–Walendar disease). J Matern Fetal Neonatal Med. 2011; 24(1):195.
[6] Neumann MM, Davio MB, Macknet MR, Applegate RL II. Dexmedetomidine for awake fibrotic intubation in a parturient with spinal muscular atrophy type III for cesarean delivery. Int J Obstet Anesth. 2009; 18(4):403-7.
[7] Habibi AS, Helsley SE, Millar S, Deballi 3rd P, Muir HA. Anesthesia for cesarean section in a patient with spinal muscular atrophy. J Clin Anesth. 2004;16(3): 217-9.
[8] Coffman JC, Fiorini K, Ristev G, Beeston W, Small RH. Transversus abdominis plane and ilioinguinal/ iliohypogastric blocks for cesarean delivery in a patient with type II spinal muscular atrophy. Int J Obstet Anest. 2016; 25: 79-81.
[9] Laffargue F, Boulot P, Lafont L, Jonquet O, Hedon B, Viala JL. An association of Werdnig-Hoffman disease and pregnancy: apropos of an unusual case. J Gynecol Obstet Biol Reprod. 1990; 19(3):321-3.
Files
IssueVol 6 No 4 (2020): Autumn QRcode
SectionCase Report(s)
DOI https://doi.org/10.18502/aacc.v6i4.4628
Keywords
Spinal muscular atrophy pregnancy anesthesia spinal

Rights and permissions
Creative Commons License This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.
How to Cite
1.
Vosoughian M, Dabir S, Dahi M, Moshari M, Tabashi S, Madadi F. Anesthetic Management of a Parturient with Spinal Muscle Atrophy for Cesarean Section: A Case Report. Arch Anesth & Crit Care. 2020;6(4):194-196.