Case Report

Anesthesia Management in Rare Case: Cutis Laxa Syndrome

Abstract

Cutis laxa is rare and hetrogenous group of disorders related to abnormalities in elastic tissue. It may be autosomal recessive, autosomal dominant, X linked or acquired. Acquired cutis laxa has developed after a febrile illness, inflammatory skin disease such a lupus eryhymatosis or erythema multiform, amyloidosis, hypersensitivity reaction to penicillin and in infants born from women who were taking penicillamine. Patients with cutis laxa have facial features,.pulmonary emphysema, cor-pulmonale, and right-sided heart failure.We present a case with cutis laxa undescended testis , and mild  pulmonary stenosis.

Sheila S. Galbraith, Disease of Dermis, Robert M. Kliegman, Nelson Textbook of Pediatric s, 20ed. Elsevier, 2011, P:3179.

Robert Sidbuy, Nelson L Turcios, Pulmonary manisfestation of dermatologic disease, Nelson L Turicious, Robert fink, pulmonary manifestation of pediatric disease, 1 st edition, Elsevier, 2009, 264-268.

Margarete R, seashore,Karen j Marcdente, Metabolic disease, marcdante Karen editor in Nelson essential of pediatric 6 th edition,Elsevier, 2010,766-69.

Andiran N, Sarikayalar F, Saraçlar M, Cağlar M. Autosomal recessive form of congenital cutis laxa: More than the clinical appearance. Pediatr Dermatol. 2002; 19:412–4.

Alan D -John Harper et al, Text book Of Pediatric. Dermatology, 3ed edition, blackwell 2011, p 652-655.

Chhabra SK, Gupta RK, Singh T. Cutis laxa & Pulmonary Emphysema. Indian J Chest Dis Allied Sci. 2001; 43(4):235-7.

Karapurkar SA, Borkar JD, Bermole BJ. Malformation of lung in neonates (lobectomy for congenital lobar emphysema and lung cyst). J Postgrad Med. 1993; 39(4):224-7.

Pandey R, Garg R, Manikandan R, Punj J, Darlong V, Singh SA. Perianesthetic management of generalized congenital cutis laxa syndrome associated with pulmonary stenosis undergoing inguinal hernia repair. Paediatr Anaesth. 2008;18(9):907-9.

A Hussain. An Anaesthetic Experience with A Rare Case Of Cutis Laxa Syndrome. Internet Journal of Anesthesiology. 2005 Volume 10 Number 2...92-952005 Volume 10 Number 2...92-95

jaculine L long,Loraine Rica,The Gale encyclopedia of Medicine: 2002, volume 2; P 978.

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IssueVol 1 No 4 (2015): Autumn QRcode
SectionCase Report(s)
Keywords
Cutis laxa pulmonary stenosis loose skin
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Creative Commons License This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.
How to Cite
1.
Maleki A, Ebrahim Soltani A, Goudarzi M, Yaghooti AA, Ostad Alipour A, Espahbodi E. Anesthesia Management in Rare Case: Cutis Laxa Syndrome. Arch Anesth & Crit Care. 2015;1(4):139-140.