Anesthesia and Airway Management of a Patient with Sturge- Weber Syndrome Associated with Extreme Ocular Manifestations and Giant Facial Hemangioma

Mahtab Poor Zamany Nejat Kermany; Badiozaman Radpay

Mahtab Poor Zamany Nejat Kermany Department of Anesthesiology and Critical Care, Labbafinejad Medical Center, Shahid Beheshti Medical Center, Tehran,Iran.
Badiozaman Radpay Department of Anesthesiology and Critical Care, Shohada Tajrish Medical Center, Shahid Beheshti Medical Center, Tehran, Iran

Keywords: sturge–weber syndrome, airway management, hemangioma

Abstract

Sturge-Weber syndrome (SWS) is a very rare congenital disorder that is manifested by facial capillary malformation (port wine stain) which may be associated with capillary – venous malformations affecting many parts such as the brain, eyes facial skin and mucosa and also airways. In this report we present an unusual 28 years old female case of SWS that presented with signs and symptoms of sudden increased intra ocular pressure (exacerbation of glaucoma) and manifestations of facial and airway involvement. A discussion about anesthetic and airway management of such patient follow the case presentation.

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